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Double compression oesotracheale fatale vasculaire et neurofibromateuse

Fischberg, C ; Cotting, J ; Hack, I ; Laurini, Ricardo LU and Payot, M (1996) In Archives de Pédiatrie 3(12). p.1253-1257
Abstract
BACKGROUND: Vascular rings are a classical cause of tracheal and esophagus compression. We report the case of such an abnormality in an infant with neurofibromatosis. CASE REPORT: A 1 week-old male infant with a familial neurofibromatosis presented a stridor with severe respiratory distress. A vascular ring was demonstrated and operated on. The stridor persisted after surgery. A postoperative oesophagogram and tracheobronchoscopy showed an irregular compression of the oesophageal lumen, thought to be due to a residual extrinsic compression. Because the postoperative echocardiogram showed an extensive tumoral infiltration of both auricles, it was decided to not operate again the child. The postmortem examination revealed a disseminated... (More)
BACKGROUND: Vascular rings are a classical cause of tracheal and esophagus compression. We report the case of such an abnormality in an infant with neurofibromatosis. CASE REPORT: A 1 week-old male infant with a familial neurofibromatosis presented a stridor with severe respiratory distress. A vascular ring was demonstrated and operated on. The stridor persisted after surgery. A postoperative oesophagogram and tracheobronchoscopy showed an irregular compression of the oesophageal lumen, thought to be due to a residual extrinsic compression. Because the postoperative echocardiogram showed an extensive tumoral infiltration of both auricles, it was decided to not operate again the child. The postmortem examination revealed a disseminated neurofibromatosis infiltrating trachea, bronchi and also the wall of esophagus. CONCLUSION: Persisting stridor and oesotracheal compression postoperatively requires search for another cause. Association of vascular ring and neurofibromatosis is probably not fortuitous. (Less)
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author
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publishing date
type
Contribution to journal
publication status
published
subject
in
Archives de Pédiatrie
volume
3
issue
12
pages
1253 - 1257
publisher
Elsevier
external identifiers
  • pmid:9033791
  • scopus:0030446739
ISSN
0929-693X
DOI
10.1016/S0929-693X(97)85937-4
language
English
LU publication?
no
id
23e69c48-68be-405c-badb-f7395f88646d (old id 1111093)
date added to LUP
2016-04-01 17:11:33
date last changed
2022-01-29 01:00:56
@article{23e69c48-68be-405c-badb-f7395f88646d,
  abstract     = {{BACKGROUND: Vascular rings are a classical cause of tracheal and esophagus compression. We report the case of such an abnormality in an infant with neurofibromatosis. CASE REPORT: A 1 week-old male infant with a familial neurofibromatosis presented a stridor with severe respiratory distress. A vascular ring was demonstrated and operated on. The stridor persisted after surgery. A postoperative oesophagogram and tracheobronchoscopy showed an irregular compression of the oesophageal lumen, thought to be due to a residual extrinsic compression. Because the postoperative echocardiogram showed an extensive tumoral infiltration of both auricles, it was decided to not operate again the child. The postmortem examination revealed a disseminated neurofibromatosis infiltrating trachea, bronchi and also the wall of esophagus. CONCLUSION: Persisting stridor and oesotracheal compression postoperatively requires search for another cause. Association of vascular ring and neurofibromatosis is probably not fortuitous.}},
  author       = {{Fischberg, C and Cotting, J and Hack, I and Laurini, Ricardo and Payot, M}},
  issn         = {{0929-693X}},
  language     = {{eng}},
  number       = {{12}},
  pages        = {{1253--1257}},
  publisher    = {{Elsevier}},
  series       = {{Archives de Pédiatrie}},
  title        = {{Double compression oesotracheale fatale vasculaire et neurofibromateuse}},
  url          = {{http://dx.doi.org/10.1016/S0929-693X(97)85937-4}},
  doi          = {{10.1016/S0929-693X(97)85937-4}},
  volume       = {{3}},
  year         = {{1996}},
}