Toward a biological definition of neuronal and glial synucleinopathies
(2025) In Nature Medicine 31(2). p.396-408- Abstract
Cerebral accumulation of alpha-synuclein (αSyn) aggregates is the hallmark event in a group of neurodegenerative diseases—collectively called synucleinopathies—which include Parkinson’s disease, dementia with Lewy bodies and multiple system atrophy. Currently, these are diagnosed by their clinical symptoms and definitively confirmed postmortem by the presence of αSyn deposits in the brain. Here, we summarize the drawbacks of the current clinical definition of synucleinopathies and outline the rationale for moving toward an earlier, biology-anchored definition of these disorders, with or without the presence of clinical symptoms. We underscore the utility of the αSyn seed amplification assay to detect aggregated αSyn in living patients... (More)
Cerebral accumulation of alpha-synuclein (αSyn) aggregates is the hallmark event in a group of neurodegenerative diseases—collectively called synucleinopathies—which include Parkinson’s disease, dementia with Lewy bodies and multiple system atrophy. Currently, these are diagnosed by their clinical symptoms and definitively confirmed postmortem by the presence of αSyn deposits in the brain. Here, we summarize the drawbacks of the current clinical definition of synucleinopathies and outline the rationale for moving toward an earlier, biology-anchored definition of these disorders, with or without the presence of clinical symptoms. We underscore the utility of the αSyn seed amplification assay to detect aggregated αSyn in living patients and to differentiate between neuronal or glial αSyn pathology. We anticipate that a biological definition of synucleinopathies, if well-integrated with the current clinical classifications, will enable further understanding of the disease pathogenesis and contribute to the development of effective, disease-modifying therapies.
(Less)
- author
- Soto, Claudio
; Mollenhauer, Brit
; Hansson, Oskar
LU
; Kang, Un Jung ; Alcalay, Roy N. ; Standaert, David ; Trenkwalder, Claudia ; Marek, Kenneth ; Galasko, Douglas and Poston, Kathleen
- organization
- publishing date
- 2025-02
- type
- Contribution to journal
- publication status
- published
- subject
- in
- Nature Medicine
- volume
- 31
- issue
- 2
- article number
- 34
- pages
- 13 pages
- publisher
- Nature Publishing Group
- external identifiers
-
- scopus:85217249905
- pmid:39885358
- ISSN
- 1078-8956
- DOI
- 10.1038/s41591-024-03469-7
- language
- English
- LU publication?
- yes
- id
- 05a95577-27f6-4726-abaf-32ccf0399ccb
- date added to LUP
- 2025-04-09 11:05:27
- date last changed
- 2025-07-17 02:33:34
@article{05a95577-27f6-4726-abaf-32ccf0399ccb, abstract = {{<p>Cerebral accumulation of alpha-synuclein (αSyn) aggregates is the hallmark event in a group of neurodegenerative diseases—collectively called synucleinopathies—which include Parkinson’s disease, dementia with Lewy bodies and multiple system atrophy. Currently, these are diagnosed by their clinical symptoms and definitively confirmed postmortem by the presence of αSyn deposits in the brain. Here, we summarize the drawbacks of the current clinical definition of synucleinopathies and outline the rationale for moving toward an earlier, biology-anchored definition of these disorders, with or without the presence of clinical symptoms. We underscore the utility of the αSyn seed amplification assay to detect aggregated αSyn in living patients and to differentiate between neuronal or glial αSyn pathology. We anticipate that a biological definition of synucleinopathies, if well-integrated with the current clinical classifications, will enable further understanding of the disease pathogenesis and contribute to the development of effective, disease-modifying therapies.</p>}}, author = {{Soto, Claudio and Mollenhauer, Brit and Hansson, Oskar and Kang, Un Jung and Alcalay, Roy N. and Standaert, David and Trenkwalder, Claudia and Marek, Kenneth and Galasko, Douglas and Poston, Kathleen}}, issn = {{1078-8956}}, language = {{eng}}, number = {{2}}, pages = {{396--408}}, publisher = {{Nature Publishing Group}}, series = {{Nature Medicine}}, title = {{Toward a biological definition of neuronal and glial synucleinopathies}}, url = {{http://dx.doi.org/10.1038/s41591-024-03469-7}}, doi = {{10.1038/s41591-024-03469-7}}, volume = {{31}}, year = {{2025}}, }