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Whole body composition analysis by the BodPod air-displacement plethysmography method in children with Phenylketonuria shows a higher body fat percentage

Albersen, Monique ; Bonthuis, Marjolein ; De Roos, Nicole M. ; Van Den Hurk, Dorine A.M. ; Carbasius Weber, Ems ; Hendriks, Margriet M.W.B. ; De Sain-Van Der Velden, Monique G.M. ; De Koning, Tom J. LU and Visser, Gepke (2010) In Journal of Inherited Metabolic Disease 33(SUPPL. 3).
Abstract

Background Phenylketonuria (PKU) causes irreversible central nervous system damage unless a phenylalanine (PHE) restricted diet with amino acid supplementation is maintained. To prevent growth retardation, a protein/amino acid intake beyond the recommended dietary protein allowance is mandatory. However, data regarding disease and/or diet related changes in body composition are inconclusive and retarded growth and/or adiposity is still reported. The BodPod whole body air-displacement plethysmography method is a fast, safe and accurate technique to measure body composition. Aim To gain more insight into the body composition of children with PKU. Methods Patients diagnosed with PKU born between 1991 and 2001 were included. Patients were... (More)

Background Phenylketonuria (PKU) causes irreversible central nervous system damage unless a phenylalanine (PHE) restricted diet with amino acid supplementation is maintained. To prevent growth retardation, a protein/amino acid intake beyond the recommended dietary protein allowance is mandatory. However, data regarding disease and/or diet related changes in body composition are inconclusive and retarded growth and/or adiposity is still reported. The BodPod whole body air-displacement plethysmography method is a fast, safe and accurate technique to measure body composition. Aim To gain more insight into the body composition of children with PKU. Methods Patients diagnosed with PKU born between 1991 and 2001 were included. Patients were identified by neonatal screening and treated in our centre. Body composition was measured using the BodPod system (Life Measurement Incorporation

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publishing date
type
Contribution to journal
publication status
published
subject
in
Journal of Inherited Metabolic Disease
volume
33
issue
SUPPL. 3
publisher
Springer
external identifiers
  • scopus:84897927846
  • pmid:20574715
ISSN
0141-8955
DOI
10.1007/s10545-010-9149-8
language
English
LU publication?
no
id
1012179e-ae1a-41a8-9fc8-7d65fdc309d5
date added to LUP
2020-02-26 10:21:39
date last changed
2024-05-29 10:05:30
@article{1012179e-ae1a-41a8-9fc8-7d65fdc309d5,
  abstract     = {{<p>Background Phenylketonuria (PKU) causes irreversible central nervous system damage unless a phenylalanine (PHE) restricted diet with amino acid supplementation is maintained. To prevent growth retardation, a protein/amino acid intake beyond the recommended dietary protein allowance is mandatory. However, data regarding disease and/or diet related changes in body composition are inconclusive and retarded growth and/or adiposity is still reported. The BodPod whole body air-displacement plethysmography method is a fast, safe and accurate technique to measure body composition. Aim To gain more insight into the body composition of children with PKU. Methods Patients diagnosed with PKU born between 1991 and 2001 were included. Patients were identified by neonatal screening and treated in our centre. Body composition was measured using the BodPod system (Life Measurement Incorporation</p>}},
  author       = {{Albersen, Monique and Bonthuis, Marjolein and De Roos, Nicole M. and Van Den Hurk, Dorine A.M. and Carbasius Weber, Ems and Hendriks, Margriet M.W.B. and De Sain-Van Der Velden, Monique G.M. and De Koning, Tom J. and Visser, Gepke}},
  issn         = {{0141-8955}},
  language     = {{eng}},
  month        = {{01}},
  number       = {{SUPPL. 3}},
  publisher    = {{Springer}},
  series       = {{Journal of Inherited Metabolic Disease}},
  title        = {{Whole body composition analysis by the BodPod air-displacement plethysmography method in children with Phenylketonuria shows a higher body fat percentage}},
  url          = {{http://dx.doi.org/10.1007/s10545-010-9149-8}},
  doi          = {{10.1007/s10545-010-9149-8}},
  volume       = {{33}},
  year         = {{2010}},
}