Double compression oesotracheale fatale vasculaire et neurofibromateuse
(1996) In Archives de Pédiatrie 3(12). p.1253-1257- Abstract
- BACKGROUND: Vascular rings are a classical cause of tracheal and esophagus compression. We report the case of such an abnormality in an infant with neurofibromatosis. CASE REPORT: A 1 week-old male infant with a familial neurofibromatosis presented a stridor with severe respiratory distress. A vascular ring was demonstrated and operated on. The stridor persisted after surgery. A postoperative oesophagogram and tracheobronchoscopy showed an irregular compression of the oesophageal lumen, thought to be due to a residual extrinsic compression. Because the postoperative echocardiogram showed an extensive tumoral infiltration of both auricles, it was decided to not operate again the child. The postmortem examination revealed a disseminated... (More)
- BACKGROUND: Vascular rings are a classical cause of tracheal and esophagus compression. We report the case of such an abnormality in an infant with neurofibromatosis. CASE REPORT: A 1 week-old male infant with a familial neurofibromatosis presented a stridor with severe respiratory distress. A vascular ring was demonstrated and operated on. The stridor persisted after surgery. A postoperative oesophagogram and tracheobronchoscopy showed an irregular compression of the oesophageal lumen, thought to be due to a residual extrinsic compression. Because the postoperative echocardiogram showed an extensive tumoral infiltration of both auricles, it was decided to not operate again the child. The postmortem examination revealed a disseminated neurofibromatosis infiltrating trachea, bronchi and also the wall of esophagus. CONCLUSION: Persisting stridor and oesotracheal compression postoperatively requires search for another cause. Association of vascular ring and neurofibromatosis is probably not fortuitous. (Less)
Please use this url to cite or link to this publication:
https://lup.lub.lu.se/record/1111093
- author
- Fischberg, C ; Cotting, J ; Hack, I ; Laurini, Ricardo LU and Payot, M
- publishing date
- 1996
- type
- Contribution to journal
- publication status
- published
- subject
- in
- Archives de Pédiatrie
- volume
- 3
- issue
- 12
- pages
- 1253 - 1257
- publisher
- Elsevier
- external identifiers
-
- pmid:9033791
- scopus:0030446739
- ISSN
- 0929-693X
- DOI
- 10.1016/S0929-693X(97)85937-4
- language
- English
- LU publication?
- no
- id
- 23e69c48-68be-405c-badb-f7395f88646d (old id 1111093)
- date added to LUP
- 2016-04-01 17:11:33
- date last changed
- 2022-01-29 01:00:56
@article{23e69c48-68be-405c-badb-f7395f88646d, abstract = {{BACKGROUND: Vascular rings are a classical cause of tracheal and esophagus compression. We report the case of such an abnormality in an infant with neurofibromatosis. CASE REPORT: A 1 week-old male infant with a familial neurofibromatosis presented a stridor with severe respiratory distress. A vascular ring was demonstrated and operated on. The stridor persisted after surgery. A postoperative oesophagogram and tracheobronchoscopy showed an irregular compression of the oesophageal lumen, thought to be due to a residual extrinsic compression. Because the postoperative echocardiogram showed an extensive tumoral infiltration of both auricles, it was decided to not operate again the child. The postmortem examination revealed a disseminated neurofibromatosis infiltrating trachea, bronchi and also the wall of esophagus. CONCLUSION: Persisting stridor and oesotracheal compression postoperatively requires search for another cause. Association of vascular ring and neurofibromatosis is probably not fortuitous.}}, author = {{Fischberg, C and Cotting, J and Hack, I and Laurini, Ricardo and Payot, M}}, issn = {{0929-693X}}, language = {{eng}}, number = {{12}}, pages = {{1253--1257}}, publisher = {{Elsevier}}, series = {{Archives de Pédiatrie}}, title = {{Double compression oesotracheale fatale vasculaire et neurofibromateuse}}, url = {{http://dx.doi.org/10.1016/S0929-693X(97)85937-4}}, doi = {{10.1016/S0929-693X(97)85937-4}}, volume = {{3}}, year = {{1996}}, }