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Double compression oesotracheale fatale vasculaire et neurofibromateuse

Fischberg, C; Cotting, J; Hack, I; Laurini, Ricardo LU and Payot, M (1996) In Archives de Pédiatrie 3(12). p.1253-1257
Abstract
BACKGROUND: Vascular rings are a classical cause of tracheal and esophagus compression. We report the case of such an abnormality in an infant with neurofibromatosis. CASE REPORT: A 1 week-old male infant with a familial neurofibromatosis presented a stridor with severe respiratory distress. A vascular ring was demonstrated and operated on. The stridor persisted after surgery. A postoperative oesophagogram and tracheobronchoscopy showed an irregular compression of the oesophageal lumen, thought to be due to a residual extrinsic compression. Because the postoperative echocardiogram showed an extensive tumoral infiltration of both auricles, it was decided to not operate again the child. The postmortem examination revealed a disseminated... (More)
BACKGROUND: Vascular rings are a classical cause of tracheal and esophagus compression. We report the case of such an abnormality in an infant with neurofibromatosis. CASE REPORT: A 1 week-old male infant with a familial neurofibromatosis presented a stridor with severe respiratory distress. A vascular ring was demonstrated and operated on. The stridor persisted after surgery. A postoperative oesophagogram and tracheobronchoscopy showed an irregular compression of the oesophageal lumen, thought to be due to a residual extrinsic compression. Because the postoperative echocardiogram showed an extensive tumoral infiltration of both auricles, it was decided to not operate again the child. The postmortem examination revealed a disseminated neurofibromatosis infiltrating trachea, bronchi and also the wall of esophagus. CONCLUSION: Persisting stridor and oesotracheal compression postoperatively requires search for another cause. Association of vascular ring and neurofibromatosis is probably not fortuitous. (Less)
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author
publishing date
type
Contribution to journal
publication status
published
subject
in
Archives de Pédiatrie
volume
3
issue
12
pages
1253 - 1257
publisher
Elsevier
external identifiers
  • pmid:9033791
  • scopus:0030446739
ISSN
0929-693X
DOI
10.1016/S0929-693X(97)85937-4
language
English
LU publication?
no
id
23e69c48-68be-405c-badb-f7395f88646d (old id 1111093)
date added to LUP
2008-07-23 09:30:14
date last changed
2017-01-01 07:26:49
@article{23e69c48-68be-405c-badb-f7395f88646d,
  abstract     = {BACKGROUND: Vascular rings are a classical cause of tracheal and esophagus compression. We report the case of such an abnormality in an infant with neurofibromatosis. CASE REPORT: A 1 week-old male infant with a familial neurofibromatosis presented a stridor with severe respiratory distress. A vascular ring was demonstrated and operated on. The stridor persisted after surgery. A postoperative oesophagogram and tracheobronchoscopy showed an irregular compression of the oesophageal lumen, thought to be due to a residual extrinsic compression. Because the postoperative echocardiogram showed an extensive tumoral infiltration of both auricles, it was decided to not operate again the child. The postmortem examination revealed a disseminated neurofibromatosis infiltrating trachea, bronchi and also the wall of esophagus. CONCLUSION: Persisting stridor and oesotracheal compression postoperatively requires search for another cause. Association of vascular ring and neurofibromatosis is probably not fortuitous.},
  author       = {Fischberg, C and Cotting, J and Hack, I and Laurini, Ricardo and Payot, M},
  issn         = {0929-693X},
  language     = {eng},
  number       = {12},
  pages        = {1253--1257},
  publisher    = {Elsevier},
  series       = {Archives de Pédiatrie},
  title        = {Double compression oesotracheale fatale vasculaire et neurofibromateuse},
  url          = {http://dx.doi.org/10.1016/S0929-693X(97)85937-4},
  volume       = {3},
  year         = {1996},
}