Advanced

Dilatation idiopathique de l'oreillette droite simulant une maladie d'Ebstein. A propos d'un cas decouvert in utero

Reinhardt-Owlya, L; Sekarski, N; Hurni, M; Laurini, Ricardo LU and Payot, M (1998) In Archives des Maladies du Cœur et des Vaisseaux 91(5). p.645-649
Abstract
In October 1992, severe dilatation of the right atrium was detected in a 35 week foetus. The septal leaflet of the tricuspid valve seemed to be displaced distally causing massive tricuspid regurgitation. The diagnosis of Ebstein's anomaly was made and confirmed after birth. Refractory right heart failure occurred at the age of 10 months and the little girl was operated. At surgery, the right atrium was very dilated; the tricuspid valve was normally positioned and was normally constituted. The right atrial wall, partially resected, contained few muscular fibres and showed patchy fibroelastosis. Four years after surgery, the child remains asymptomatic. Dilatation of the right atrium and the tricuspid annulus caused pseudo-displacement of the... (More)
In October 1992, severe dilatation of the right atrium was detected in a 35 week foetus. The septal leaflet of the tricuspid valve seemed to be displaced distally causing massive tricuspid regurgitation. The diagnosis of Ebstein's anomaly was made and confirmed after birth. Refractory right heart failure occurred at the age of 10 months and the little girl was operated. At surgery, the right atrium was very dilated; the tricuspid valve was normally positioned and was normally constituted. The right atrial wall, partially resected, contained few muscular fibres and showed patchy fibroelastosis. Four years after surgery, the child remains asymptomatic. Dilatation of the right atrium and the tricuspid annulus caused pseudo-displacement of the septal leaflet of the tricuspid valve. This, combined with the importance of tricuspid regurgitation, led to the erroneous diagnosis of Ebstein's anomaly. It is important to differentiate idiopathic right atrial dilatation from Ebstein's anomaly because surgery is much more difficult in the latter case. (Less)
Please use this url to cite or link to this publication:
author
alternative title
Idiopathic dilatation of the right atrium simulating Ebstein's anomaly. Apropos of a case diagnosed in utero
publishing date
type
Contribution to journal
publication status
published
subject
in
Archives des Maladies du Cœur et des Vaisseaux
volume
91
issue
5
pages
645 - 649
publisher
Baillière Tindall
external identifiers
  • pmid:9749217
  • scopus:0031809948
ISSN
0003-9683
language
French
LU publication?
no
id
84819e8d-1100-41db-afac-f5a5940b4932 (old id 1113988)
date added to LUP
2008-07-16 14:41:04
date last changed
2017-01-01 06:56:37
@article{84819e8d-1100-41db-afac-f5a5940b4932,
  abstract     = {In October 1992, severe dilatation of the right atrium was detected in a 35 week foetus. The septal leaflet of the tricuspid valve seemed to be displaced distally causing massive tricuspid regurgitation. The diagnosis of Ebstein's anomaly was made and confirmed after birth. Refractory right heart failure occurred at the age of 10 months and the little girl was operated. At surgery, the right atrium was very dilated; the tricuspid valve was normally positioned and was normally constituted. The right atrial wall, partially resected, contained few muscular fibres and showed patchy fibroelastosis. Four years after surgery, the child remains asymptomatic. Dilatation of the right atrium and the tricuspid annulus caused pseudo-displacement of the septal leaflet of the tricuspid valve. This, combined with the importance of tricuspid regurgitation, led to the erroneous diagnosis of Ebstein's anomaly. It is important to differentiate idiopathic right atrial dilatation from Ebstein's anomaly because surgery is much more difficult in the latter case.},
  author       = {Reinhardt-Owlya, L and Sekarski, N and Hurni, M and Laurini, Ricardo and Payot, M},
  issn         = {0003-9683},
  language     = {fre},
  number       = {5},
  pages        = {645--649},
  publisher    = {Baillière Tindall},
  series       = {Archives des Maladies du Cœur et des Vaisseaux},
  title        = {Dilatation idiopathique de l'oreillette droite simulant une maladie d'Ebstein. A propos d'un cas decouvert in utero},
  volume       = {91},
  year         = {1998},
}