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Nordic Haemophilia Council's Practical Guidelines on Diagnosis and Management of von Willebrand Disease

Lassila, Riitta; Holme, Pal Andre; Landorph, Andrea; Petrini, Pia; Onundarson, Pall T. and Hillarp, Andreas LU (2011) In Seminars in Thrombosis and Hemostasis 37(5). p.495-502
Abstract
von Willebrand disease (VWD) is the most common inherited bleeding disorder characterized by spontaneous or tissue injury related, mostly mucocutaneous, bleeding events. VWD affects both males and females and is caused by quantitative or qualitative deficiency of von Willebrand factor. The diagnostic procedure is complicated because VWD is highly heterogeneous, and differential diagnosis from platelet disorders may be challenging. Moreover, these defects may even coexist, impacting the bleeding phenotype. Mild and moderate VWD can be difficult to distinguish from the normal population, and VWD subtyping may also be problematic. This article summarizes the guidelines of the Nordic Haemophilia Council (NHC), which are intended to serve as a... (More)
von Willebrand disease (VWD) is the most common inherited bleeding disorder characterized by spontaneous or tissue injury related, mostly mucocutaneous, bleeding events. VWD affects both males and females and is caused by quantitative or qualitative deficiency of von Willebrand factor. The diagnostic procedure is complicated because VWD is highly heterogeneous, and differential diagnosis from platelet disorders may be challenging. Moreover, these defects may even coexist, impacting the bleeding phenotype. Mild and moderate VWD can be difficult to distinguish from the normal population, and VWD subtyping may also be problematic. This article summarizes the guidelines of the Nordic Haemophilia Council (NHC), which are intended to serve as a practical tool and provide the standards for diagnosing and treating VWD patients. The complete Nordic Guidelines on VWD are available at the NHC Web site (http://nordhemophilia.org). (Less)
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author
organization
publishing date
type
Contribution to journal
publication status
published
subject
keywords
von Willebrand disease, Nordic Haemophilia Council, Guidelines
in
Seminars in Thrombosis and Hemostasis
volume
37
issue
5
pages
495 - 502
publisher
Georg Thieme Verlag
external identifiers
  • wos:000295698300011
  • scopus:81755171930
ISSN
1098-9064
DOI
10.1055/s-0031-1281034
language
English
LU publication?
yes
id
07bbfd6b-a910-4bdf-82ff-c973aaa52707 (old id 2212187)
date added to LUP
2011-12-01 08:31:55
date last changed
2017-08-13 04:02:18
@article{07bbfd6b-a910-4bdf-82ff-c973aaa52707,
  abstract     = {von Willebrand disease (VWD) is the most common inherited bleeding disorder characterized by spontaneous or tissue injury related, mostly mucocutaneous, bleeding events. VWD affects both males and females and is caused by quantitative or qualitative deficiency of von Willebrand factor. The diagnostic procedure is complicated because VWD is highly heterogeneous, and differential diagnosis from platelet disorders may be challenging. Moreover, these defects may even coexist, impacting the bleeding phenotype. Mild and moderate VWD can be difficult to distinguish from the normal population, and VWD subtyping may also be problematic. This article summarizes the guidelines of the Nordic Haemophilia Council (NHC), which are intended to serve as a practical tool and provide the standards for diagnosing and treating VWD patients. The complete Nordic Guidelines on VWD are available at the NHC Web site (http://nordhemophilia.org).},
  author       = {Lassila, Riitta and Holme, Pal Andre and Landorph, Andrea and Petrini, Pia and Onundarson, Pall T. and Hillarp, Andreas},
  issn         = {1098-9064},
  keyword      = {von Willebrand disease,Nordic Haemophilia Council,Guidelines},
  language     = {eng},
  number       = {5},
  pages        = {495--502},
  publisher    = {Georg Thieme Verlag},
  series       = {Seminars in Thrombosis and Hemostasis},
  title        = {Nordic Haemophilia Council's Practical Guidelines on Diagnosis and Management of von Willebrand Disease},
  url          = {http://dx.doi.org/10.1055/s-0031-1281034},
  volume       = {37},
  year         = {2011},
}