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Cardiac rhabdomyoma mimicking haemodynamics of hypoplastic left heart syndrome

El-Segaier, Milad LU and Galal, Mohammed O. (2014) In Acta Cardiologica 69(3). p.308-310
Abstract
Cardiac rhabdonnyomas are rare and often regress spontaneously. However, the management of rhabdomyoma with severe inflow and outflow obstructions is a challenge. An infant with a massive left ventricular rhabdomyoma mimicking the haemodynamics of hypoplastic left heart syndrome is reported. Surgery could not be contemplated because the mitral valve leaflets and chordae were imbedded in the tumour mass. The arterial duct (AD) was kept open to perfuse the systemic circulation and palliations with pulmonary artery branch banding and AD stenting were planned. However; while waiting for spontaneous regression of the tumour, the child died of circulatory collapse when 4 weeks old.
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author
organization
publishing date
type
Contribution to journal
publication status
published
subject
keywords
Rhabdomyoma, spontaneous regression, mitral obstruction
in
Acta Cardiologica
volume
69
issue
3
pages
308 - 310
publisher
Acta Cardiologica
external identifiers
  • wos:000346681300010
  • scopus:84902765833
ISSN
0001-5385
DOI
10.2143/AC.69.3.3027834
language
English
LU publication?
yes
id
164c7e62-5243-46b0-82f2-b8a155d66f51 (old id 4941507)
date added to LUP
2015-02-03 07:08:48
date last changed
2017-01-01 05:26:51
@article{164c7e62-5243-46b0-82f2-b8a155d66f51,
  abstract     = {Cardiac rhabdonnyomas are rare and often regress spontaneously. However, the management of rhabdomyoma with severe inflow and outflow obstructions is a challenge. An infant with a massive left ventricular rhabdomyoma mimicking the haemodynamics of hypoplastic left heart syndrome is reported. Surgery could not be contemplated because the mitral valve leaflets and chordae were imbedded in the tumour mass. The arterial duct (AD) was kept open to perfuse the systemic circulation and palliations with pulmonary artery branch banding and AD stenting were planned. However; while waiting for spontaneous regression of the tumour, the child died of circulatory collapse when 4 weeks old.},
  author       = {El-Segaier, Milad and Galal, Mohammed O.},
  issn         = {0001-5385},
  keyword      = {Rhabdomyoma,spontaneous regression,mitral obstruction},
  language     = {eng},
  number       = {3},
  pages        = {308--310},
  publisher    = {Acta Cardiologica},
  series       = {Acta Cardiologica},
  title        = {Cardiac rhabdomyoma mimicking haemodynamics of hypoplastic left heart syndrome},
  url          = {http://dx.doi.org/10.2143/AC.69.3.3027834},
  volume       = {69},
  year         = {2014},
}