Intestinal Lymphangiectasia
(2025) p.379-390- Abstract
Endoscopically, the villi of the small bowel in intestinal lymphangiectasia typically appear white and may be swollen. Less commonly, tiny white spots are visible in the mucosa. The whitish discoloration of the villi is caused by chylomicrons, which accumulate in and obstruct the dilated lymphatic capillaries. These changes can also be demonstrated histologically. Lymphangiectasia is characterized endoscopically as localized, patchy, or diffuse. Diffuse lymphangiectasia causes the mucosa to appear “snow-covered” or “dusted with powdered sugar” at endoscopy. Functional lymphangiectasia is dependent on food intake and appears to have no pathologic significance. Primary intestinal lymphangiectasias is a very rare hereditary disease with... (More)
Endoscopically, the villi of the small bowel in intestinal lymphangiectasia typically appear white and may be swollen. Less commonly, tiny white spots are visible in the mucosa. The whitish discoloration of the villi is caused by chylomicrons, which accumulate in and obstruct the dilated lymphatic capillaries. These changes can also be demonstrated histologically. Lymphangiectasia is characterized endoscopically as localized, patchy, or diffuse. Diffuse lymphangiectasia causes the mucosa to appear “snow-covered” or “dusted with powdered sugar” at endoscopy. Functional lymphangiectasia is dependent on food intake and appears to have no pathologic significance. Primary intestinal lymphangiectasias is a very rare hereditary disease with severe exudative enteropathy Secondary lymphangiectasia is an accompanying feature of many different underlying intestinal and extraintestinal diseases of inflammatory, malignant, iatrogenic origin or as part of a syndrome.
(Less)
- author
- Wiedbrauck, Felix ; Toth, Ervin LU and Wurm Johansson, Gabriele LU
- organization
- publishing date
- 2025
- type
- Chapter in Book/Report/Conference proceeding
- publication status
- published
- subject
- keywords
- Capsule endoscopy, Enteroscopy, Lymphangiectasia, Protein-losing enteropathy, Small bowel, Waldmann disease, Yellow nail syndrome
- host publication
- Video Capsule Endoscopy : Atlas and Reference Guide to Capsule and Small Bowel Endoscopy - Atlas and Reference Guide to Capsule and Small Bowel Endoscopy
- edition
- 2nd
- pages
- 12 pages
- publisher
- Springer Science and Business Media B.V.
- external identifiers
-
- scopus:105023351162
- ISBN
- 9783031647185
- 9783031647192
- DOI
- 10.1007/978-3-031-64719-2_28
- language
- English
- LU publication?
- yes
- id
- 4db44328-1f25-4ef0-933a-ecb12fc4aadf
- date added to LUP
- 2026-02-03 17:23:55
- date last changed
- 2026-02-03 17:24:15
@inbook{4db44328-1f25-4ef0-933a-ecb12fc4aadf,
abstract = {{<p>Endoscopically, the villi of the small bowel in intestinal lymphangiectasia typically appear white and may be swollen. Less commonly, tiny white spots are visible in the mucosa. The whitish discoloration of the villi is caused by chylomicrons, which accumulate in and obstruct the dilated lymphatic capillaries. These changes can also be demonstrated histologically. Lymphangiectasia is characterized endoscopically as localized, patchy, or diffuse. Diffuse lymphangiectasia causes the mucosa to appear “snow-covered” or “dusted with powdered sugar” at endoscopy. Functional lymphangiectasia is dependent on food intake and appears to have no pathologic significance. Primary intestinal lymphangiectasias is a very rare hereditary disease with severe exudative enteropathy Secondary lymphangiectasia is an accompanying feature of many different underlying intestinal and extraintestinal diseases of inflammatory, malignant, iatrogenic origin or as part of a syndrome.</p>}},
author = {{Wiedbrauck, Felix and Toth, Ervin and Wurm Johansson, Gabriele}},
booktitle = {{Video Capsule Endoscopy : Atlas and Reference Guide to Capsule and Small Bowel Endoscopy}},
isbn = {{9783031647185}},
keywords = {{Capsule endoscopy; Enteroscopy; Lymphangiectasia; Protein-losing enteropathy; Small bowel; Waldmann disease; Yellow nail syndrome}},
language = {{eng}},
pages = {{379--390}},
publisher = {{Springer Science and Business Media B.V.}},
title = {{Intestinal Lymphangiectasia}},
url = {{http://dx.doi.org/10.1007/978-3-031-64719-2_28}},
doi = {{10.1007/978-3-031-64719-2_28}},
year = {{2025}},
}