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Congenital absence of the intrahepatic portion of the portal vein in an adult male resected for hepatocellular carcinoma

Lundstedt, C. LU ; Lindell, G. LU ; Tranberg, K. G. LU and Svartholm, E. (2001) In European Radiology 11(11). p.2228-2231
Abstract

We report a case of congenital absence of the portal vein (CAPV) in an adult male who underwent resection for hepatocellular carcinoma. CAPV is a rare anomaly; only 29 cases, mostly in children, have been presented to date. An association between CAPV and cardiac abnormalities, polysplenia syndrome, skeletal abnormalities and liver tumors has been seen in children. To the best of our knowledge this is the first case of CAPV in an adult male resected for hepatocellular carcinoma. However, since CAPV can be without symptoms, the number of undiagnosed cases is not known.

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author
publishing date
type
Contribution to journal
publication status
published
subject
keywords
Congenital absence of portal vein, Hepatocellular carcinoma, Liver vascular supply, Portal vein anomalies
in
European Radiology
volume
11
issue
11
pages
4 pages
publisher
Springer
external identifiers
  • scopus:0034753337
  • pmid:11702163
ISSN
0938-7994
DOI
10.1007/s003300100833
language
English
LU publication?
no
id
d21afee7-fb6a-424b-bd10-128b3c0a9aaa
date added to LUP
2019-06-15 16:40:20
date last changed
2020-01-13 02:01:34
@article{d21afee7-fb6a-424b-bd10-128b3c0a9aaa,
  abstract     = {<p>We report a case of congenital absence of the portal vein (CAPV) in an adult male who underwent resection for hepatocellular carcinoma. CAPV is a rare anomaly; only 29 cases, mostly in children, have been presented to date. An association between CAPV and cardiac abnormalities, polysplenia syndrome, skeletal abnormalities and liver tumors has been seen in children. To the best of our knowledge this is the first case of CAPV in an adult male resected for hepatocellular carcinoma. However, since CAPV can be without symptoms, the number of undiagnosed cases is not known.</p>},
  author       = {Lundstedt, C. and Lindell, G. and Tranberg, K. G. and Svartholm, E.},
  issn         = {0938-7994},
  language     = {eng},
  month        = {01},
  number       = {11},
  pages        = {2228--2231},
  publisher    = {Springer},
  series       = {European Radiology},
  title        = {Congenital absence of the intrahepatic portion of the portal vein in an adult male resected for hepatocellular carcinoma},
  url          = {http://dx.doi.org/10.1007/s003300100833},
  doi          = {10.1007/s003300100833},
  volume       = {11},
  year         = {2001},
}