Stress granules : emerging players in neurodegenerative diseases
(2025) In Translational Neurodegeneration 14(1).- Abstract
Stress granules (SGs) are membraneless organelles formed in the cellular cytoplasm under stressful conditions through liquid–liquid phase separation (LLPS). SG assembly can be both dependent and independent of the eIF2α pathway, whereas cellular protein quality control systems mediate SG disassembly. Chaperones and specific domains of RNA-binding proteins strongly contribute to the regulation SG dynamics. Chronic stress, arising in association with aging, may promote persistent SGs that are difficult to disassemble, thereby acting as a potential pathological nidus for protein aggregation in neurodegenerative diseases (NDDs). In this review, we discuss the dynamics of SGs and the factors involved with SG assembly and disassembly. We also... (More)
Stress granules (SGs) are membraneless organelles formed in the cellular cytoplasm under stressful conditions through liquid–liquid phase separation (LLPS). SG assembly can be both dependent and independent of the eIF2α pathway, whereas cellular protein quality control systems mediate SG disassembly. Chaperones and specific domains of RNA-binding proteins strongly contribute to the regulation SG dynamics. Chronic stress, arising in association with aging, may promote persistent SGs that are difficult to disassemble, thereby acting as a potential pathological nidus for protein aggregation in neurodegenerative diseases (NDDs). In this review, we discuss the dynamics of SGs and the factors involved with SG assembly and disassembly. We also highlight the relationship among LLPS, SGs, and the pathogenesis of different NDDs. More importantly, we summarize SG assembly-disassembly, which may be a double-edged sword in the pathophysiology of NDDs. This review aims to provide new insights into the biology and pathology of LLPS, SGs, and NDDs.
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- author
- Yuan, Lin ; Mao, Li Hong ; Huang, Yong Ye ; Outeiro, Tiago F. ; Li, Wen LU ; Vieira, Tuane C.R.G. and Li, Jia Yi LU
- organization
- publishing date
- 2025-12
- type
- Contribution to journal
- publication status
- published
- subject
- keywords
- Liquid–liquid phase separation, Neurodegenerative disease, RNA-binding protein, Stress granules
- in
- Translational Neurodegeneration
- volume
- 14
- issue
- 1
- article number
- 22
- publisher
- BioMed Central (BMC)
- external identifiers
-
- scopus:105004738191
- pmid:40355949
- ISSN
- 2047-9158
- DOI
- 10.1186/s40035-025-00482-9
- language
- English
- LU publication?
- yes
- id
- 02aab798-fc1f-402d-b724-9bf975e2bb06
- date added to LUP
- 2025-07-14 11:17:36
- date last changed
- 2025-07-15 03:00:10
@article{02aab798-fc1f-402d-b724-9bf975e2bb06, abstract = {{<p>Stress granules (SGs) are membraneless organelles formed in the cellular cytoplasm under stressful conditions through liquid–liquid phase separation (LLPS). SG assembly can be both dependent and independent of the eIF2α pathway, whereas cellular protein quality control systems mediate SG disassembly. Chaperones and specific domains of RNA-binding proteins strongly contribute to the regulation SG dynamics. Chronic stress, arising in association with aging, may promote persistent SGs that are difficult to disassemble, thereby acting as a potential pathological nidus for protein aggregation in neurodegenerative diseases (NDDs). In this review, we discuss the dynamics of SGs and the factors involved with SG assembly and disassembly. We also highlight the relationship among LLPS, SGs, and the pathogenesis of different NDDs. More importantly, we summarize SG assembly-disassembly, which may be a double-edged sword in the pathophysiology of NDDs. This review aims to provide new insights into the biology and pathology of LLPS, SGs, and NDDs.</p>}}, author = {{Yuan, Lin and Mao, Li Hong and Huang, Yong Ye and Outeiro, Tiago F. and Li, Wen and Vieira, Tuane C.R.G. and Li, Jia Yi}}, issn = {{2047-9158}}, keywords = {{Liquid–liquid phase separation; Neurodegenerative disease; RNA-binding protein; Stress granules}}, language = {{eng}}, number = {{1}}, publisher = {{BioMed Central (BMC)}}, series = {{Translational Neurodegeneration}}, title = {{Stress granules : emerging players in neurodegenerative diseases}}, url = {{http://dx.doi.org/10.1186/s40035-025-00482-9}}, doi = {{10.1186/s40035-025-00482-9}}, volume = {{14}}, year = {{2025}}, }