Advanced

Hepatocellular carcinoma associated with arteriohepatic dysplasia in a 4-year-old girl

Békássy, Albert LU ; Garwicz, Stanislaw LU ; Wiebe, Thomas LU ; Hägerstrand, Inga and Jensen, Ove A (1992) In Medical and Pediatric Oncology 20(1). p.78-83
Abstract
Hepatocellular carcinoma and obliterated hepatic bile duct were found at postmortem examination in a 4-year-old girl with arteriohepatic dysplasia (Alagille's syndrome). AFP level was extremely high. Liver cirrhosis was present on percutaneous needle biopsy 9 months before she succumbed in progressive liver failure. Episodes of repeated gastrointestinal, life-threatening hemorrhages occurred during the last 6 months of her life. Histopathologic findings of the eyes were documented at autopsy.
Please use this url to cite or link to this publication:
author
organization
publishing date
type
Contribution to journal
publication status
published
subject
keywords
Alagille's syndrome, child, hepatic carcinoma, liver cirrhosis, biliary atresia, autopsy, histopathology, eyes, liver, AFP
in
Medical and Pediatric Oncology
volume
20
issue
1
pages
78 - 83
publisher
John Wiley & Sons
external identifiers
  • pmid:1309208
  • scopus:0026571153
ISSN
1096-911X
DOI
10.1002/mpo.2950200118
language
English
LU publication?
yes
id
1f170dc1-8f38-415c-9f89-f96ec6570889 (old id 1106244)
date added to LUP
2008-07-31 10:06:58
date last changed
2017-07-09 03:35:43
@article{1f170dc1-8f38-415c-9f89-f96ec6570889,
  abstract     = {Hepatocellular carcinoma and obliterated hepatic bile duct were found at postmortem examination in a 4-year-old girl with arteriohepatic dysplasia (Alagille's syndrome). AFP level was extremely high. Liver cirrhosis was present on percutaneous needle biopsy 9 months before she succumbed in progressive liver failure. Episodes of repeated gastrointestinal, life-threatening hemorrhages occurred during the last 6 months of her life. Histopathologic findings of the eyes were documented at autopsy.},
  author       = {Békássy, Albert and Garwicz, Stanislaw and Wiebe, Thomas and Hägerstrand, Inga and Jensen, Ove A},
  issn         = {1096-911X},
  keyword      = {Alagille's syndrome,child,hepatic carcinoma,liver cirrhosis,biliary atresia,autopsy,histopathology,eyes,liver,AFP},
  language     = {eng},
  number       = {1},
  pages        = {78--83},
  publisher    = {John Wiley & Sons},
  series       = {Medical and Pediatric Oncology},
  title        = {Hepatocellular carcinoma associated with arteriohepatic dysplasia in a 4-year-old girl},
  url          = {http://dx.doi.org/10.1002/mpo.2950200118},
  volume       = {20},
  year         = {1992},
}