Mondini-like malformation mimicking otosclerosis and superior semicircular canal dehiscence.
(2006) In Journal of Laryngology and Otology 120(5). p.419-422- Abstract
- In 2003, it was reported that superior semicircular canal dehiscence can mimic otosclerosis because of low-frequency bone conduction hearing gain and dissipation of air-conducted acoustic energy through the dehiscence. We report the case of a 17-year-old girl with left-sided combined hearing loss thought to be due to otosclerosis. Bone conduction thresholds were -10 dB at 250 and 500 Hz and she had a 40 dB air bone gap at 250 Hz. When a tuning fork was placed at her ankle she heard it in her left ear. Acoustic reflexes and vestibular evoked myogenic potentials could be elicited bilaterally. Imaging of the temporal bones showed no otosclerosis, superior semicircular canal dehiscence or large vestibular aqueduct, but a left-sided,... (More)
- In 2003, it was reported that superior semicircular canal dehiscence can mimic otosclerosis because of low-frequency bone conduction hearing gain and dissipation of air-conducted acoustic energy through the dehiscence. We report the case of a 17-year-old girl with left-sided combined hearing loss thought to be due to otosclerosis. Bone conduction thresholds were -10 dB at 250 and 500 Hz and she had a 40 dB air bone gap at 250 Hz. When a tuning fork was placed at her ankle she heard it in her left ear. Acoustic reflexes and vestibular evoked myogenic potentials could be elicited bilaterally. Imaging of the temporal bones showed no otosclerosis, superior semicircular canal dehiscence or large vestibular aqueduct, but a left-sided, Mondini-like dysplasia of the cochlea with a modiolar deficiency could be seen. Mondini-like cochlear dysplasia should be added to the causes of inner-ear conductive hearing loss. (Less)
Please use this url to cite or link to this publication:
https://lup.lub.lu.se/record/154453
- author
- Karlberg, Mikael LU ; Annertz, Mårten LU and Magnusson, Måns LU
- organization
- publishing date
- 2006
- type
- Contribution to journal
- publication status
- published
- subject
- keywords
- hearing loss, cochlear diseases, vestibular function tests, conductive
- in
- Journal of Laryngology and Otology
- volume
- 120
- issue
- 5
- pages
- 419 - 422
- publisher
- Cambridge University Press
- external identifiers
-
- wos:000238243300017
- pmid:16556352
- scopus:33748751296
- pmid:16556352
- ISSN
- 1748-5460
- DOI
- 10.1017/S0022215106000934
- language
- English
- LU publication?
- yes
- id
- 6ba54da4-2fea-46ef-9b92-66ef745c56df (old id 154453)
- alternative location
- http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=PubMed&list_uids=16556352&dopt=Abstract
- date added to LUP
- 2016-04-01 11:56:34
- date last changed
- 2022-01-26 20:32:47
@article{6ba54da4-2fea-46ef-9b92-66ef745c56df, abstract = {{In 2003, it was reported that superior semicircular canal dehiscence can mimic otosclerosis because of low-frequency bone conduction hearing gain and dissipation of air-conducted acoustic energy through the dehiscence. We report the case of a 17-year-old girl with left-sided combined hearing loss thought to be due to otosclerosis. Bone conduction thresholds were -10 dB at 250 and 500 Hz and she had a 40 dB air bone gap at 250 Hz. When a tuning fork was placed at her ankle she heard it in her left ear. Acoustic reflexes and vestibular evoked myogenic potentials could be elicited bilaterally. Imaging of the temporal bones showed no otosclerosis, superior semicircular canal dehiscence or large vestibular aqueduct, but a left-sided, Mondini-like dysplasia of the cochlea with a modiolar deficiency could be seen. Mondini-like cochlear dysplasia should be added to the causes of inner-ear conductive hearing loss.}}, author = {{Karlberg, Mikael and Annertz, Mårten and Magnusson, Måns}}, issn = {{1748-5460}}, keywords = {{hearing loss; cochlear diseases; vestibular function tests; conductive}}, language = {{eng}}, number = {{5}}, pages = {{419--422}}, publisher = {{Cambridge University Press}}, series = {{Journal of Laryngology and Otology}}, title = {{Mondini-like malformation mimicking otosclerosis and superior semicircular canal dehiscence.}}, url = {{http://dx.doi.org/10.1017/S0022215106000934}}, doi = {{10.1017/S0022215106000934}}, volume = {{120}}, year = {{2006}}, }