Differential memory enrichment of cytotoxic CD4 T cells in Parkinson’s disease patients reactive to α-synuclein
(2025) In npj Parkinson's Disease 11(1).- Abstract
Parkinson’s disease (PD) is a complex neurodegenerative disease with a largely unknown etiology. Although the loss of dopaminergic neurons in the substantia nigra pars compacta is the pathological hallmark of PD, neuroinflammation also plays a fundamental role in PD pathology. We have previously reported that PD patients have increased frequencies of T cells reactive to peptides from α-synuclein (α-syn). However, not all PD participants respond to α-syn. Furthermore, we have previously found that CD4 T cells from PD participants responding to α-syn (PD_R) are transcriptionally distinct from PD participants not responding to α-syn (PD_NR). To gain further insight into the pathology of PD_R participants, we investigated surface protein... (More)
Parkinson’s disease (PD) is a complex neurodegenerative disease with a largely unknown etiology. Although the loss of dopaminergic neurons in the substantia nigra pars compacta is the pathological hallmark of PD, neuroinflammation also plays a fundamental role in PD pathology. We have previously reported that PD patients have increased frequencies of T cells reactive to peptides from α-synuclein (α-syn). However, not all PD participants respond to α-syn. Furthermore, we have previously found that CD4 T cells from PD participants responding to α-syn (PD_R) are transcriptionally distinct from PD participants not responding to α-syn (PD_NR). To gain further insight into the pathology of PD_R participants, we investigated surface protein expression of 11 proteins whose genes had previously been found to be differentially expressed when comparing PD_R and healthy control participants not responding to α-syn (HC_NR). We found that Cadherin EGF LAG seven-pass G-type receptor 2 (CELSR2) was expressed on a significantly higher proportion of CD4 effector memory T cells (TEM) in PD_R compared to HC_NR. Single-cell RNA sequencing analysis of cells expressing or not expressing CELSR2 revealed that PD_R participants have elevated frequencies of activated TEM subsets and an almost complete loss of cytotoxic TEM cells. Flow cytometry analyses confirmed that Granulysin+ CD4 cytotoxic TEM cells are reduced in PD_R. Taken together, these results provide further insight into the perturbation of T cell subsets in PD_R, and highlights the need for further investigation into the role of Granulysin+ CD4 cytotoxic TEM in PD pathology.
(Less)
- author
- Freuchet, Antoine
; Johansson, Emil
LU
; Frazier, April ; Litvan, Irene ; Goldman, Jennifer G. ; Alcalay, Roy N. ; Sulzer, David ; Lindestam Arlehamn, Cecilia S. and Sette, Alessandro
- organization
- publishing date
- 2025-12
- type
- Contribution to journal
- publication status
- published
- subject
- in
- npj Parkinson's Disease
- volume
- 11
- issue
- 1
- article number
- 127
- publisher
- Springer Nature
- external identifiers
-
- scopus:105005409895
- ISSN
- 2373-8057
- DOI
- 10.1038/s41531-025-00981-6
- language
- English
- LU publication?
- yes
- id
- 424899c0-5e96-45c4-9b2e-6a59a88bf5b7
- date added to LUP
- 2025-07-14 10:53:46
- date last changed
- 2025-07-14 10:54:09
@article{424899c0-5e96-45c4-9b2e-6a59a88bf5b7, abstract = {{<p>Parkinson’s disease (PD) is a complex neurodegenerative disease with a largely unknown etiology. Although the loss of dopaminergic neurons in the substantia nigra pars compacta is the pathological hallmark of PD, neuroinflammation also plays a fundamental role in PD pathology. We have previously reported that PD patients have increased frequencies of T cells reactive to peptides from α-synuclein (α-syn). However, not all PD participants respond to α-syn. Furthermore, we have previously found that CD4 T cells from PD participants responding to α-syn (PD_R) are transcriptionally distinct from PD participants not responding to α-syn (PD_NR). To gain further insight into the pathology of PD_R participants, we investigated surface protein expression of 11 proteins whose genes had previously been found to be differentially expressed when comparing PD_R and healthy control participants not responding to α-syn (HC_NR). We found that Cadherin EGF LAG seven-pass G-type receptor 2 (CELSR2) was expressed on a significantly higher proportion of CD4 effector memory T cells (T<sub>EM</sub>) in PD_R compared to HC_NR. Single-cell RNA sequencing analysis of cells expressing or not expressing CELSR2 revealed that PD_R participants have elevated frequencies of activated T<sub>EM</sub> subsets and an almost complete loss of cytotoxic T<sub>EM</sub> cells. Flow cytometry analyses confirmed that Granulysin<sup>+</sup> CD4 cytotoxic T<sub>EM</sub> cells are reduced in PD_R. Taken together, these results provide further insight into the perturbation of T cell subsets in PD_R, and highlights the need for further investigation into the role of Granulysin<sup>+</sup> CD4 cytotoxic T<sub>EM</sub> in PD pathology.</p>}}, author = {{Freuchet, Antoine and Johansson, Emil and Frazier, April and Litvan, Irene and Goldman, Jennifer G. and Alcalay, Roy N. and Sulzer, David and Lindestam Arlehamn, Cecilia S. and Sette, Alessandro}}, issn = {{2373-8057}}, language = {{eng}}, number = {{1}}, publisher = {{Springer Nature}}, series = {{npj Parkinson's Disease}}, title = {{Differential memory enrichment of cytotoxic CD4 T cells in Parkinson’s disease patients reactive to α-synuclein}}, url = {{http://dx.doi.org/10.1038/s41531-025-00981-6}}, doi = {{10.1038/s41531-025-00981-6}}, volume = {{11}}, year = {{2025}}, }