Clinical Management and Transplant Considerations in Pediatric Pulmonary Hypertension Due to Left Heart Disease : A Scientific Statement From the American Heart Association
(2024) In Circulation. Heart failure- Abstract
Children with left heart disease are at risk for developing pulmonary hypertension, initially secondary to pulmonary venous hypertension that can progress to include elevated pulmonary vascular resistance, known as combined pre- and postcapillary pulmonary hypertension. Elevated pulmonary vascular resistance may pose a risk to the right ventricle of a newly transplanted heart because of increased afterload and is an important consideration for heart transplant eligibility. However, the epidemiology, pathophysiology, optimal diagnostic and treatment approaches, and thresholds for pulmonary vascular resistance in pulmonary hypertension associated with left heart disease remain unclear because of lack of evidence, particularly in... (More)
Children with left heart disease are at risk for developing pulmonary hypertension, initially secondary to pulmonary venous hypertension that can progress to include elevated pulmonary vascular resistance, known as combined pre- and postcapillary pulmonary hypertension. Elevated pulmonary vascular resistance may pose a risk to the right ventricle of a newly transplanted heart because of increased afterload and is an important consideration for heart transplant eligibility. However, the epidemiology, pathophysiology, optimal diagnostic and treatment approaches, and thresholds for pulmonary vascular resistance in pulmonary hypertension associated with left heart disease remain unclear because of lack of evidence, particularly in pediatrics. The result is heterogeneity with respect to hemodynamic assessment, use of pulmonary vasodilator therapies, and heart transplant listing. This scientific statement aims to synthesize the available data and highlight areas of general consensus as well as important knowledge gaps.
(Less)
- author
- Hopper, Rachel K
; Hansmann, Georg
; Hollander, Seth A
; Dipchand, Anne I
; van der Have, Oscar
LU
; Iler, Colleen ; Herrington, Cynthia ; Rosenzweig, Erika B ; Alejos, Juan C and Tran-Lundmark, Karin LU
- author collaboration
- organization
- publishing date
- 2024-12-09
- type
- Contribution to journal
- publication status
- epub
- subject
- in
- Circulation. Heart failure
- article number
- e000086
- publisher
- American Heart Association
- external identifiers
-
- scopus:85212140298
- pmid:39648916
- ISSN
- 1941-3297
- DOI
- 10.1161/HHF.0000000000000086
- language
- English
- LU publication?
- yes
- id
- dfa681cd-3aff-4895-9642-d444181ee1b3
- date added to LUP
- 2024-12-11 14:24:18
- date last changed
- 2025-07-10 11:52:49
@article{dfa681cd-3aff-4895-9642-d444181ee1b3, abstract = {{<p>Children with left heart disease are at risk for developing pulmonary hypertension, initially secondary to pulmonary venous hypertension that can progress to include elevated pulmonary vascular resistance, known as combined pre- and postcapillary pulmonary hypertension. Elevated pulmonary vascular resistance may pose a risk to the right ventricle of a newly transplanted heart because of increased afterload and is an important consideration for heart transplant eligibility. However, the epidemiology, pathophysiology, optimal diagnostic and treatment approaches, and thresholds for pulmonary vascular resistance in pulmonary hypertension associated with left heart disease remain unclear because of lack of evidence, particularly in pediatrics. The result is heterogeneity with respect to hemodynamic assessment, use of pulmonary vasodilator therapies, and heart transplant listing. This scientific statement aims to synthesize the available data and highlight areas of general consensus as well as important knowledge gaps.</p>}}, author = {{Hopper, Rachel K and Hansmann, Georg and Hollander, Seth A and Dipchand, Anne I and van der Have, Oscar and Iler, Colleen and Herrington, Cynthia and Rosenzweig, Erika B and Alejos, Juan C and Tran-Lundmark, Karin}}, issn = {{1941-3297}}, language = {{eng}}, month = {{12}}, publisher = {{American Heart Association}}, series = {{Circulation. Heart failure}}, title = {{Clinical Management and Transplant Considerations in Pediatric Pulmonary Hypertension Due to Left Heart Disease : A Scientific Statement From the American Heart Association}}, url = {{http://dx.doi.org/10.1161/HHF.0000000000000086}}, doi = {{10.1161/HHF.0000000000000086}}, year = {{2024}}, }