Marco Maccarana (Former)
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- 2021
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Inhibition of iduronic acid biosynthesis by ebselen reduces glycosaminoglycan accumulation in mucopolysaccharidosis type I fibroblasts
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- Contribution to journal › Article
- 2019
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Recombinant dermatan sulfate is a potent activator of heparin cofactor II-dependent inhibition of thrombin
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- Contribution to journal › Article
- 2018
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Dermatan sulfate epimerase 1 and dermatan 4-O-sulfotransferase 1 form complexes that generate long epimerized 4-O-sulfated blocks
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- Contribution to journal › Article
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Mark
Dendritic cell migration to skin-draining lymph nodes is controlled by dermatan sulfate and determines adaptive immunity magnitude
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- Contribution to journal › Article
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Three unreported cases of TMEM199-CDG, a rare genetic liver disease with abnormal glycosylation
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- Contribution to journal › Article
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Gene expression of the two developmentally regulated dermatan sulfate epimerases in the Xenopus embryo
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- Contribution to journal › Article
- 2017
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Increased deposition of glycosaminoglycans and altered structure of heparan sulfate in idiopathic pulmonary fibrosis
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- Contribution to journal › Article
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Fibromodulin deficiency reduces collagen structural network but not glycosaminoglycan content in a syngeneic model of colon carcinoma
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- Contribution to journal › Article
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Asporin-deficient mice have tougher skin and altered skin glycosaminoglycan content and structure
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- Contribution to journal › Article
- 2016
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Mark
Deciphering the mode of action of the processive polysaccharide modifying enzyme dermatan sulfate epimerase 1 by hydrogen-deuterium exchange mass spectrometry
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- Contribution to journal › Article
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The tyrosine kinase inhibitor imatinib augments extracellular fluid exchange and reduces average collagen fibril diameter in experimental carcinoma
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- Contribution to journal › Article
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Drugs affecting glycosaminoglycan metabolism
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- Contribution to journal › Scientific review
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Mark
Musculocontractural Ehlers-Danlos syndrome and neurocristopathies : Dermatan sulfate is required for Xenopus neural crest cells to migrate and adhere to fibronectin
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- Contribution to journal › Article
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Mark
Determination of Autosomal Dominant or Recessive Methionine Adenosyltransferase I/III Deficiencies Based on Clinical and Molecular Studies.
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- Contribution to journal › Article
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Mark
Aberrant neural crest development causes craniofacial and other malformations in an animal model of Musculocontractural Ehlers-Danlos syndrome.
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- Contribution to journal › Scientific review
- 2015
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Dermatan Sulfate-Free Mice Display Embryological Defects and Are Neonatal Lethal Despite Normal Lymphoid and Non-Lymphoid Organogenesis.
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- Contribution to journal › Article
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Mark
PAPST1 regulates sulfation of heparan sulfate proteoglycans in epithelial MDCK II cells.
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- Contribution to journal › Article
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Mark
The serpin PN1 is a feedback regulator of FGF signaling in germ layer and primary axis formation.
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- Contribution to journal › Article
- 2014
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Mark
Dermatan sulfate epimerase 1 deficient mice as a model for human abdominal wall defects.
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- Contribution to journal › Article
- 2013
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Mark
Iduronic Acid in chondroitin/dermatan sulfate affects directional migration of aortic smooth muscle cells.
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- Contribution to journal › Article